Patients diagnosed with parapsoriasis and treated with phototherapy puva or uvbnb were selected. The prognosis of smallplaque parapsoriasis is generally good. These lesions, called plaques, may be irregularly roundshaped to oval and are 10 cm 4 in or larger in diameter. Parapsoriasis describes a group of skin diseases that can be characterized by scaly patches or slightly elevated papules andor plaques red, scaly patches that have a resemblance to psoriasis. Young male with long standing erythematosquamous lesions. However, this description includes several inflammatory cutaneous diseases that are unrelated with respect to pathogenesis, histopathology, an.
Parapsoriasis en plaques ubersicht altmeyers enzyklopadie. They are considered to be lymphoproliferative in origin, as a number of patients progress to cutaneous tcell lymphoma or mycosis fungoides. Parapsoriasis genetic and rare diseases information. We evaluated the efficacy of phototherapy in the treatment of parapsoriasis and its relation with tccl. Parapsoriasis is a peculiar reaction pattern of the skin that appears to have a spectrum with small plaque parapsoriasis at one end and large plaque at the other. Parapsoriasis describes a group of cutaneous diseases that can be characterized by scaly patches or slightly elevated papules andor plaques that have a resemblance to psoriasishence the nomenclature. About forty years has passed since brocq united under the name parapsoriasis a group of diseases belonging to. However, it is not known whether the early stage of ctcl can be distinguished from parapsoriasis en plaques. Parapsoriasis retiforme extensa o micosis fungoide. Letiopathogenie des parapsoriasis en gouttes ppg n. Largeplaque parapsoriasis is a common associate of retiform. Xanthoerythrodermia perstans is a distinct variant with lesions that are yellow in color 452. The term parapsoriasis was used by brocq 1902 to group a number of conditions previously described under different names.
Patients diagnosed with parapsoriasis and treated with phototherapy puva or. Large plaque parapsoriasis are skin lesions that may be included in the modern scheme of cutaneous conditions described as parapsoriasis. An evaluation of the treatment of parapsoriasis with. Plaque parapsoriasis is a skin condition that resembles psoriasis. Jan, 2019 the prognosis of smallplaque parapsoriasis is generally good. They can be very thin plaques that are asymptomatic or mildly pruritic. Parapsoriasis trastornos dermatologicos manual msd version. Genotypic pattern observed in small plaque parapsoriasis is similar to that observed in chronic dermatitis, and the pattern of clonality of t cells is consistent with the response of a specific subset of t cells that have been stimulated by an antigen. Parapsoriasis en plaques benigne kleinherdige altmeyers. Age and sex distribution smallplaque parapsoriasis is a rare skin condition that is typically seen in middleaged to older adults in the age group of 3060 years.
However, this description includes several inflammatory cutaneous diseases that are unrelated with respect to pathogenesis, histopathology, and response to treatment. The term parapsoriasis refers to a heterogeneous group of uncommon dermatoses occurring mainly in older adults and characterized by erythematous and scaly patches of variable size, chronic course, and resistance to treatment. For language access assistance, contact the ncats public information officer. Parapsoriasis en plaque brocq, largeplaque type, parapsoriasis en plaque brocq, large focal type, parapsoriasis en grandes plaques, premalignant form of parapsoriasis en plaque. Interestingly, two of these lesions with a benign phenotype parapsoriasis en plaque and dermatitis were taken from a patient who was diagnosed with tcell lymphoma 89 years later. Occasion may arise when nothing is more difficult in dermatology than a differentiation between parapsoriasis and allied conditions which are similar both clinically and histologically.
It is caused by an abnormal inflammation of the skin. Differential diagnosis of parapsoriasis jama dermatology. Chronic superficial scaly dermatitis cssd is an uncommon chronic skin condition characterised by round or oval red, slightly scaly patches on limbs and trunk. About forty years has passed since brocq united under the name parapsoriasis a. Parapsoriasis definition of parapsoriasis by medical. Parapsoriasis genetic and rare diseases information center. Small plaque parapsoriasis characteristically occurs with skin lesions that are round, oval, discrete patches or thin plaques, mainly on the trunk 452. Es reconocida por su erupcion roja, fina y brillante. Article in french bonvalet d, colaugohm k, belaich s, civatte j, degos r. The topic parapsoriasis en plaques you are seeking is a synonym, or alternative name, or is closely related to the medical condition largeplaque parapsoriasis. Jul 08, 2014 if you have problems viewing pdf files, download the latest version of adobe reader.
Parapsoriasis definition of parapsoriasis by medical dictionary. Parapsoriasis describes a group of cutaneous diseases that can be characterized by scaly patches or slightly elevated papules andor plaques dispersed on the trunk or proximal extremities that have a resemblance to psoriasishence the nomenclature. The skin lesions appear as scaly patches and plaques. Parapsoriasis is a term encompassing several disorders of the skin that possess a similar clinical presentation to psoriasis. Abstract parapsoriasis en plaques largeplaque type is a premalignant condition capable of developing into cutaneous tcell lymphoma ctcl. Descargue como ppt, pdf, txt o lea en linea desde scribd. Xanthoerythrodermia perstans is a distinct variant with lesions that are yellow in color 452 digitate dermatosis is a distinct variant with lesions in the shape of a finger and distributed symmetrically on the flanks. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 toll free. Parapsoriasis en plaque definition of parapsoriasis en.
Parapsoriasis symptoms, causes, diagnosis, and treatment information for parapsoriasis parapsoriasis with alternative diagnoses, fulltext book chapters, misdiagnosis, research. Otros diagnosticos diferenciales incluyen eccema cronico, eccematide y psoriasis. Muche jm, lukowsky a, heim j, friedrich m, audring h, sterry w 1999 demonstration of frequent occurrence of clonal t cells in the peripheral blood but not in the skin of patients with small plaque parapsoriasis. Parapsoriasis is an etiologically heterogeneous group of disorders that tend to have a similar appearancethin, scaling, dull, pink patches and plaques with a. Parapsoriasis is an etiologically heterogeneous group of disorders that tend to have a similar appearancethin, scaling, dull, pink patches and plaques with a slightly atrophic or wrinkled appearance. Muche jm, lukowsky a, heim j, friedrich m, audring h, sterry w 1999 demonstration of frequent occurrence of clonal t cells in the peripheral blood but not in. It is also known as chronic superficial dermatitis, small plaque parapsoriasis and digitate dermatosis. Whether parapsoriasis represents an early stage of tcell cutaneous lymphoma is still the subject of controversy. Confusingly, the term parapsoriasis en plaque has been used for either spp or lpp. Les parapsoriasis peuvent avoir une evolution chronique, avec poussees et remissions setalant sur quelques semaines a plusieurs annees. Other conditions sometimes grouped under the banner of parapsoriasis are pityriasis lichenoides et varioliformis acuta, pityriasis lichenoides chronica, and lymphomatoid papulosis, all. Other conditions sometimes grouped under the banner of parapsoriasis are pityriasis lichenoides et varioliformis acuta, pityriasis lichenoides chronica, and lymphomatoid papulosis, all of which are the subjects of separate chapters. Dermis parapsoriasis en plaque brocq, largeplaque type. Parapsoriasis symptoms, causes, diagnosis, and treatment information for parapsoriasis parapsoriasis with alternative diagnoses, fulltext book chapters, misdiagnosis, research treatments, prevention, and prognosis.
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